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성인에서 발생한 Glomerulocystic Kidney Disease 1예 |
정소영 , 이진헌 , 송현용 , 강신욱 , 최규헌 , 이호영 , 한대석 , 정현주 , 최인준 , 김명진 , 이종태 |
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Abstract |
Glomerulocystic kidney disease(GCKD) is an uncommon type of renal cystic disease charaeterized by dilatation of Bowmans space with variable atro- phy of glomerular tuft. GCKD is not widely recognized as a condition thst affect adults, because most of the patients were neonate or infants with other associated congenital abnormalities in other organs. We experienced a case of GCKD in a 40 year-old woman who was admitted because of seizure attack and severe reanal failure. Abdominal ultrasonography and computed tomography revealed numerous small cysts confined to the renal cortex and renal biopsy specimen showed cystic dilatation of Bowmans space with atrophic glomerular tuft. She also had a family history on cystic renal disease. A GCKD can be considered as a cause of renal dysfunction in adult patients having enlarged kidneys. |
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