Immunoglobulin G4 Related Retroperitoneal Fibrosis with Acute Kidney Injury: Report of A Case |
Yoon Ji Kim, M.D.1, Jin Uk Jeong, M.D.1, Mi-Jung Kim, M.D.2, Eun Kyoung Lee, M.D.3, Hyun Woo Kim, M.D.4 and Jai Won Chang, M.D.1 |
Department of Internal Medicine1 and Pathology2 College of Medicine University of Ulsan, Asan Medical Center, Seoul, Korea, Department of Internal Medicine3 College of Medicine, Dankook University, Cheonan, Korea, Department of Internal Medicine4 College of Medicine, Cheju National University, Cheju, Korea |
증례 : 면역글로불린 G4와 연관된 후복막 섬유증으로 인한 급성 신손상 1예 |
김윤지1 , 정진욱1 , 김미정2 , 이은경3 , 김현우4 , 장재원1 |
울산대학교 의과대학 서울아산병원 내과학교실1 , 병리학교실2, 단국대학교 의과대학 내과학교실3 , 제주대학교 의과대학 내과학교실4 |
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Abstract |
Immunoglobuin G4 (IgG4)-related sclerosing disease is a recently recognized syndrome characterized clinically by male predominance, elevated serum IgG4 level, and good response to steroid therapy.
The pathologic characteristics are extensive lymphoplasmacytic infiltration with IgG4- positive cell and irregular fibrosis in various organs (pancreas, bile duct, salivary gland, retroperitoneum, kidney and lung). Some inflammatory pseudotumors may be involved in this disease. Herein, we experienced a case of IgG4-related retroperitoneal fibrosis with postrenal acute kidney injury and inflammatory pseudotumor of thyroid in a 31-year-old female who underwent insertion of double J catheter at both ureters and received corticosteroid treatment. |
Key Words:
Acute renal failure, Immunoglobulin G, Inflammatory pseudotumor, Retroperitoneal fibrosis |
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