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| 심한 소화관 침범 ,다발성 장막염 ( 흉수 , 복수 ) 수신증을 동반한 전신성 괴사성 혈관염 1예 |
| 장세호 , 김윤구 , 고은미 , 이규백 , 이풍렬 , 오하영 ,서연림 , 주인욱 , 김보현 |
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| Abstract |
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The systemic necrotizing vasculitides represents a spectrum of rare disorders with shared features of vascular inflammation, vascular necrosis, and varying degrees of target-organ ischemia. Their clinical features are protean and depend on the nature and intensity of the inflammatory response and the distribution and degree of target-organ damage. They might be the only manifestation of a disease or can be a secondary component of another primary disease such as hematologic malignancy, cardiac myxorna, infection and connective tissue disease. Ascites occurs in various diseases, but it is not characteristically found in the prirnary vasculitis syndromes. Although pleuritis and pericarditis may occur in polyarieritis, peritoneal involvement has been reported only in cases with intestinal compli- cation and secondary acute abdomen. So there was some difficulty in initial diagnosis of primary vasculitis. We report a case of systemic necrotizing vasculitis with severe gastrointestinal tract involve- ment, polyserositis(pleural effusion and ascites) with- out intestinal complication and secondary acute abdomen, hydronephrosis, but successfully treated with prednisolone and cyclophosphamide. |
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